Genetics and sensorineural pathophysiology

Group leader

Miguel Ángel Moreno Pelayo

mmorenop(ELIMINAR)@salud.madrid.org

Principal Investigator

  • Francisco Javier del Castillo Fernández del Pino
  • Ignacio del Castillo Fernández del Pino
  • Matías Morín Rodríguez

Collaborating Staff

  • Yolanda Martín Santo Domingo
  • Ana María Valero Rubio
  • Manuela Villamar López
  • Verónica Barca Tierno
  • María Lachgar Ruiz
  • Concepción Villalón Villarroel
  • Eva María García Galloway
  • Patricia Fernández San José
  • Lucía Soletto Esteban
  • Irene Garcia Vaquero
  • Natalia Sannikova
  • Sandra Pérez Rial
  • Marta Pacio Mínguez
  • Patricia Rodríguez Solana
  • Elena Rodríguez de Tiedra
  • María Domínguez Ruiz
  • Irene Vázquez Domínguez
Imagen equipo

Group leader

Miguel Ángel Moreno Pelayo

mmorenop(ELIMINAR)@salud.madrid.org

Principal Investigator

  • Francisco Javier del Castillo Fernández del Pino
  • Ignacio del Castillo Fernández del Pino
  • Matías Morín Rodríguez

Collaborating Staff

  • Yolanda Martín Santo Domingo
  • Ana María Valero Rubio
  • Manuela Villamar López
  • Verónica Barca Tierno
  • María Lachgar Ruiz
  • Concepción Villalón Villarroel
  • Eva María García Galloway
  • Patricia Fernández San José
  • Lucía Soletto Esteban
  • Irene Garcia Vaquero
  • Natalia Sannikova
  • Sandra Pérez Rial
  • Marta Pacio Mínguez
  • Patricia Rodríguez Solana
  • Elena Rodríguez de Tiedra
  • María Domínguez Ruiz
  • Irene Vázquez Domínguez

Strategic objectives

  1. Identification of new genes associated with hereditary pathology in hypoacusias, pathology of the anterior segment of the eye, autoinflammatory syndromes and other rare diseases.
  2. Performance of functional assays and generation of cell and mouse models for the study of the associated mechanisms of pathogenesis.
  3. Development, validation and transfer to the market of diagnostic tools based on next-generation sequencing and microarrays.
  4. Design of clinical guidelines for the rare diseases group.

Research lines

  • Spinal muscular atrophy.
  • Genetic basis of tuberous sclerosis.
  • Genetic and molecular basis of Chiari malformation.
  • Hereditary basis of glaucoma and of the pathology of the anterior segment of the eye.
  • Hidradenitis suppurativa.
  • Hereditary hypoacusias (syndromic and non-syndromic).
  • Autoinflammatory syndromes.
  • Primary immunodeficiencies associated with the TCR/CD3 complex and DNA repair defects.
  • microRNA cure: Modulation of microRNAs to eliminate latency reservoirs in HIV-infected patients.
  • Neurofibromatosis type 1 and 2, and neuro-cardiofacial-cutaneous syndromes.
  • SAPHO syndrome (chronic recurrent multifocal osteomyelitis).

Location

Outpatient clinic building 

Ground floor
Genetics Service
Ramón y Cajal University Hospital

Keywords

rare diseases, genetic pathology, massive sequencing, microarray-based CGH, functional assays, transgenic mice